A 38 year old female presents with acute onset shortness of breath and left sided chest pain. CXR reveals a left sided pneumothorax with mediastinal shift to the right. Numerous thin walled lucencies are noted throughout both lungs.
What is the most likely diagnosis?
Correct Answer:
Lymphangiomyomatosis
Primary spontaneous pneumothorax | |
Lymphangiomyomatosis | |
Cavitating lung metastases | |
Multiple arteriovenous malformation | |
Multiple cavitating granulomata |
Lymphangiomyomatosis (LAM) is a multisystem disorder which almost exclusively affect females of child bearing age. It may occur in isolation or in association with tuberous sclerosis. Chest findings include chylous pleural effusion, hyperinflation, variable sized thin walled cysts and recurrent pneumothoraces.